Pulmonary Sequestration with aneurysmal celiac artery blood supply Coexisting with Superior Mesenteric Artery Syndrome: A case report and literature review

Rare Co-existence of Pulmonary Sequestration with Superior Mesenteric Artery Syndrome.

Abstract

Pulmonary sequestration is a rare bronchopulmonary foregut malformation characterized by the abnormal development of non-functional lung tissue enclosed by visceral pulmonary pleura, supplied by a systemic arterial blood supply, and lacking communication with the bronchial tree. The blood supply commonly arises from the thoracic or abdominal aorta. We reported a 44-year-old female who presented with vomiting and recent weight loss. The physical and biochemical examination was unremarkable. A contrast-enhanced abdominal CT scan reveals signs of superior mesenteric artery syndrome (SMA), including a decreased aortomesenteric angle and aortomesenteric distance. The lower chest sections show an irregular consolidative lesion in the posterior-medial segment of the Left lower lobe supplied by an aberrant aneurysmal vessel from the celiac artery, consistent with intralobar pulmonary sequestration (ILS). The coexistence of SMA syndrome with ILS is a novel finding, as both conditions affect organs of different locations and embryological origins.

A literature review was conducted to examine the presentation and vascular supply of ILS.